Q. Dietary modification?
Dietary modification includes nutritional support that allows normal growth and development. Plasma phenylalanine concentration between the range of 40 and 80 m mol and tyrosine concentration between 50 and 150 μ mol should be maintained. Phenylalanine - tyrosine restricted diet is advocated. Initially a hydrolysate low in phenylalanine and tyrosine is used with small amounts of milk. If there is an elevation in methiornine a synthetic mixture without tyrosine, phenylalanine and methionine should be used.