Question 1: Your patient is pre-school aged and his diet consists of low protein foods and a phenylalanine-free formula. What will you monitor and evaluate regularly to ensure the health and wellness of this child? Include at least three examples and justify your responses.
Question 2: Define inborn errors of metabolism and describe how nutrition status might be affected. What is the relationship between phenylalanine and tyrosine? How and why is this relationship disrupted with PKU? What are the consequences of untreated PKU?